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уфе","retina":false,"avatarId":"0","isMacOS":false,"brand":"alice-ru","device":{"isIOS":false,"platform":"desktop"},"expFlags":{"isFootnoteDetails":true,"isFootnoteRedesignDivided":true,"futurisMultiqueryFlag":true}},"dialogStoreProps":{"baseUrl":"","orderedPairUUID":["Question"],"requestResponsePairs":{"data":{"Question":{"userMessage":"Аутоиммунный гепатит: что это?","markdown":"**Аутоиммунный гепатит (АИГ)** — хроническое воспалительное заболевание печени, при котором иммунная система ошибочно атакует гепатоциты (клетки печени) и приводит к их разрушению, фиброзу и циррозу [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/)[2](https://doct.ru/diseases/autoimmunniy-gepatit.html)[3](https://kapmed.ru/spravochnyi-centr/stati-i-instruktsii/autoimmunnyy-gepatit/). Заболевание встречается редко (1–2 случая на 100 тыс. человек в год), чаще у женщин (соотношение 3:1) [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Без лечения постепенно прогрессирует и вызывает тяжёлые осложнения [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). При своевременной диагностике и терапии возможна длительная ремиссия [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Причины\nТочные причины АИГ неизвестны, но выделяют несколько вероятных факторов риска [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/): \n* **Генетическая предрасположенность** — связь с генами HLA (DR3 и DR4), которые регулируют иммунный ответ [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Вирусные инфекции** — запустить развитие аутоиммунного воспаления печени могут вирусы гепатита А, В, С, герпеса, кори, Эпштейна-Барра [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Приём лекарств** — применение средств, влияющих на работу иммунной системы, может быть одной из причин поражения печени [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Симптомы\nКлинические проявления АИГ разнообразны [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). У одних людей заболевание на протяжении многих лет протекает бессимптомно, у других быстро приводит к печёночной недостаточности [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Некоторые признаки: \n* общая слабость и быстрая утомляемость [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* тошнота, потеря аппетита [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* боль в правом подреберье [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* желтуха (пожелтение кожи и склер) [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* боли в мышцах и суставах [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* кожный зуд [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n\nИногда АИГ развивается остро — в этом случае по симптомам напоминает вирусный гепатит: повышается температура тела, появляется выраженная желтуха, в крови отмечают рост печёночных ферментов [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Диагностика\nДиагностику назначает терапевт, гастроэнтеролог или гепатолог [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Обследование может включать: \n* **Биохимический анализ крови** — определяют повышение АЛТ, АСТ и билирубина [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Анализы крови на антитела** — выявляют антинуклеарные антитела (ANA), антигладкомышечные антитела (SMA), печёночно-почечные (LKM) и др. [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Инструментальные методы** — ультразвуковое исследование печени, компьютерная томография (КТ) или магнитно-резонансная томография (МРТ) [11](https://shifa-msk.ru/articles/meditsinskiy-tsentr/terapiya/autoimmunnyy-gepatit-simptomy-diagnostika-i-metody-lecheniya/). \n* **Печёночная биопсия** — позволяет оценить степень воспаления и фиброза, а также подтвердить аутоиммунный характер гепатита [11](https://shifa-msk.ru/articles/meditsinskiy-tsentr/terapiya/autoimmunnyy-gepatit-simptomy-diagnostika-i-metody-lecheniya/).\n\n## Лечение\nЛечение АИГ направлено на подавление иммунного ответа, уменьшение воспаления, предотвращение прогрессирования заболевания и защиту печени от дальнейшего повреждения [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). Некоторые методы: \n* **Медикаментозная терапия** — использование кортикостероидов (например, преднизолона) и других иммуносупрессивных препаратов [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n* **Поддерживающая терапия** — диета, регулярный мониторинг состояния пациента и уровня печёночных ферментов [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n* **Хирургическое вмешательство** — в тяжёлых случаях, когда аутоиммунный гепатит приводит к необратимым изменениям в печени, может потребоваться трансплантация печени [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n\nЛечение обычно длительное и может продолжаться в течение многих лет [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). 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