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Для всех гемобластозов характерна системность поражения, по мере прогрессирования лейкозы и гематосаркомы могут трансформироваться друг в друга [2](https://yandex.ru/medicine/disease/gemoblastozy)[6](https://www.KrasotaiMedicina.ru/diseases/hematologic/hemoblastosis). \n\n**Причины** — генетические мутации в стволовых или полипотентных клетках, которые могут провоцироваться различными факторами, например: ионизирующим излучением, воздействием химических веществ, инфекциями, вызванными вирусами, генетической предрасположенностью [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz).\n\n\n\n## Классификация\nГемобластозы делятся на **два основных типа** в зависимости от локализации мутировавших клеток [2](https://yandex.ru/medicine/disease/gemoblastozy): \n1. **Лейкозы** — раковые клетки образуются в костном мозге [2](https://yandex.ru/medicine/disease/gemoblastozy)[3](https://new.nmicr.ru/pacientam/oncology/krovetvornaja-i-limfaticheskaja-sistemy/). Делятся на острые и хронические формы [2](https://yandex.ru/medicine/disease/gemoblastozy). \n2. **Лимфомы** — раковые лимфоцитарные клетки локализуются в лимфатических узлах, но в процесс могут вовлекаться другие органы [2](https://yandex.ru/medicine/disease/gemoblastozy)[3](https://new.nmicr.ru/pacientam/oncology/krovetvornaja-i-limfaticheskaja-sistemy/). Подразделяются на две большие группы — ходжкинские и неходжкинские лимфомы [2](https://yandex.ru/medicine/disease/gemoblastozy).\n\n## Симптомы\nСимптоматика гемобластозов варьируется в зависимости от формы заболевания, но выделяют несколько общих признаков [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz): \n* необъяснимая потеря веса [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz); \n* ночная потливость [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz); \n* повышенная температура тела, не имеющая очевидных инфекционных причин [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz); \n* увеличение лимфатических узлов [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz); \n* поражение костного мозга, нарушение кроветворения [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz). \n\nТакже могут быть и другие менее специфичные симптомы: анемия, иммунодефицит, нарушение свёртываемости крови, поражение костей, неврологические проявления [1](https://www.euroonco.ru/onkogematologiya/gemoblastoz).\n\n## Диагностика\nДля постановки точного диагноза рекомендуется консультация гематолога [5](https://polyclinika.ru/tech/gemoblastoz-simptomy-i-lechenie/). Некоторые методы диагностики: \n* **Анализы крови** — обращают внимание на изменение количества эритроцитов, тромбоцитов, подсчитывают лейкоциты, лимфоциты [5](https://polyclinika.ru/tech/gemoblastoz-simptomy-i-lechenie/). \n* **Пункция спинного мозга** и **биопсия увеличенных лимфоузлов** — позволяют получить цитогенетический и гистологический анализ тканей [5](https://polyclinika.ru/tech/gemoblastoz-simptomy-i-lechenie/). \n* **По показаниям** — УЗИ внутренних органов, рентгенография грудной клетки, черепа, позвоночника, костей таза, а также КТ или МРТ этих областей [5](https://polyclinika.ru/tech/gemoblastoz-simptomy-i-lechenie/).\n\n## Лечение\nЛечение гемобластозов может включать: \n* **Химиотерапию** — основной и наиболее эффективный метод лечения большинства форм гемобластозов [2](https://yandex.ru/medicine/disease/gemoblastozy). \n* **Лучевую терапию** — в некоторых случаях показано использование лучевой терапии для разрушения опухолевых клеток в определённых участках организма [2](https://yandex.ru/medicine/disease/gemoblastozy). \n* **Трансплантацию костного мозга** — при ряде агрессивных и рецидивирующих форм гемобластозов, а также при неэффективности других методов лечения [2](https://yandex.ru/medicine/disease/gemoblastozy). \n* **Таргетную терапию и иммунотерапию** — современные подходы, направленные на избирательное воздействие на опухолевые клетки с минимальным влиянием на здоровые ткани [2](https://yandex.ru/medicine/disease/gemoblastozy). \n\nКаждая схема лечения подбирается индивидуально и может меняться в зависимости от реакции пациента на терапию [2](https://yandex.ru/medicine/disease/gemoblastozy).","linksData":[{"sourceId":1,"url":"https://www.euroonco.ru/onkogematologiya/gemoblastoz","shownUrl":"https://www.euroonco.ru/onkogematologiya/gemoblastoz","title":"Гемобластозы классификация и симптомы, лечение гемобластозов в клинике 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