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Кисты постепенно увеличиваются и замещают здоровую ткань почек, что нарушает работу органа и приводит к развитию хронической болезни почек [8](https://ProBolezny.ru/polikistoz-pochek/). \n\nВыделяют два типа поликистоза почек [2](https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/): \n1. **Аутосомно-доминантный** — наиболее распространённая форма, обычно проявляется в возрасте 30–50 лет [2](https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/). \n2. **Аутосомно-рецессивный** — более редкая форма, чаще диагностируется у младенцев и детей [2](https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/).\n\n## Причины\nОсновная причина — **мутации в генах** [8](https://ProBolezny.ru/polikistoz-pochek/). В 90% случаев мутации наследственные, реже — спонтанные [3](https://www.PuchkovK.ru/urologiya/kista-pochki/polikistoz-pochek/). \n\nМутации возникают при формировании плода (внутриутробно) [8](https://ProBolezny.ru/polikistoz-pochek/).\n\n## Симптомы\nНа начальных этапах симптомы могут не проявляться — кисты небольшого размера не оказывают давления на окружающие ткани [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/). Некоторые признаки по мере увеличения кист: \n* **Повышение артериального давления**, плохо поддающееся медикаментозному контролю [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/). \n* **Боли в области поясницы**, тяжесть или тупая ноющая боль, не зависящая от физических нагрузок [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/). \n* **При развитии инфекции** (например, пиелонефрита) — резкое усиление болевого синдрома, лихорадка и ухудшение общего состояния [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/). \n* **По мере прогрессирования** — признаки почечной недостаточности: слабость, тошнота, снижение аппетита, отёчность, изменение суточного объёма мочи [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/). \n* **Иногда кисты разрываются** — это приводит к появлению крови в моче, резкой боли, напоминающей почечную колику [10](https://centr-hirurgii.ru/surgery/operativnaya-urologiya-andrologiya/polikistoz-pochek/).\n\n## Диагностика\nОсновной метод диагностики — **ультразвуковое исследование (УЗИ)**, позволяющий выявить кисты в почках, оценить их размеры и количество [12](https://fmbansk.ru/zabolevaniya/polikistoz-pochek-simptomatika-diagnostika-i-lechenie/). Иногда врач может направить на: \n* **Компьютерную томографию (КТ)** — позволяет более детально оценить структуру почек, особенно при планировании хирургического вмешательства [12](https://fmbansk.ru/zabolevaniya/polikistoz-pochek-simptomatika-diagnostika-i-lechenie/). \n* **Магнитно-резонансную томографию (МРТ)** — наиболее информативный метод, позволяющий выявить даже мелкие кисты (диаметром от 2–3 мм) [12](https://fmbansk.ru/zabolevaniya/polikistoz-pochek-simptomatika-diagnostika-i-lechenie/). \n* **Генетическое тестирование** — выявление мутаций в генах PKD1, PKD2 (при аутосомно-доминантном типе) или PKHD1 (при аутосомно-рецессивном типе) [12](https://fmbansk.ru/zabolevaniya/polikistoz-pochek-simptomatika-diagnostika-i-lechenie/).\n\n## Лечение\n**Специфического лечения, полностью излечивающего поликистоз почек, не существует** [2](https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/). Терапия направлена на замедление прогрессирования заболевания и устранение симптомов [2](https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/). Некоторые методы лечения: \n* **Медикаментозная терапия** — препараты для снижения артериального давления, антибактериальные препараты (при наличии воспалительного процесса) [13](https://www.smclinic.ru/diseases/polikistoz-pochek/). \n* **При развитии осложнений** (разрыв кист, нагноение, кровоизлияние) — оперативные методы лечения: пункция кисты под контролем УЗИ с последующим удалением её содержимого и промыванием растворами антисептиков, полостная операция — хирург производит разрез, удаляет кровь или гной из кист [13](https://www.smclinic.ru/diseases/polikistoz-pochek/). \n* **При развитии тяжёлой почечной недостаточности** — гемодиализ либо трансплантация [13](https://www.smclinic.ru/diseases/polikistoz-pochek/). \n\nПри первых признаках поликистоза почек нужно обратиться к терапевту или нефрологу [4](https://unionclinic.ru/polikistoz-pochek/).","linksData":[{"sourceId":1,"url":"https://gutaclinic.ru/articles/polikistoz-pochek/","shownUrl":"https://gutaclinic.ru/articles/polikistoz-pochek/","title":"Поликистоз почек: диагностика и лечение в статье от ГУТА КЛИНИК","shortUrl":"gutaclinic.ru","isTranslated":false,"description":"","greenUrl":"gutaclinic.ru"},{"sourceId":2,"url":"https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/","shownUrl":"https://Medgorod-clinic.ru/stati/polikistozpocheksimptomyisovremennyepodkhodyklecheniyu/","title":"Поликистоз почек: симптомы, диагностика и современные подходы к лечению.","shortUrl":"Medgorod-clinic.ru","isTranslated":false,"description":"","greenUrl":"Medgorod-clinic.ru"},{"sourceId":3,"url":"https://www.PuchkovK.ru/urologiya/kista-pochki/polikistoz-pochek/","shownUrl":"https://www.PuchkovK.ru/urologiya/kista-pochki/polikistoz-pochek/","title":"Поликистоз почек - причины, симптомы, лечение, удаление, операция. - Хирург К. 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