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Процесс сопровождается воспалением, повреждением мелких кровеносных сосудов и образованием рубцовой ткани, что ограничивает функциональность органов и тканей [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). \n\nВыделяют **системную склеродермию** — поражает не только кожу, но и внутренние органы, включая лёгкие, сердце, почки и желудочно-кишечный тракт, и **локализованную склеродермию** — поражение ограничивается кожей [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/).\n\n\n\n## Причины\nТочные причины склеродермии до сих пор неизвестны, но исследования показывают, что болезнь вызывается сочетанием генетических, иммунологических и экологических факторов [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/)[5](https://uteka.ru/articles/bolezni/sklerodermiya-prichini-simptomi-i-lechenie/). Некоторые факторы, которые могут провоцировать заболевание: \n* **Генетическая предрасположенность** — у пациентов со склеродермией часто выявляют семейные случаи аутоиммунных заболеваний [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). \n* **Иммунные нарушения** — иммунная система атакует здоровые клетки, воспринимая их как угрозу, что вызывает хроническое воспаление [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). \n* **Негативные факторы окружающей среды** — агрессивная бытовая химия, производственная пыль, пестициды и другие вещества [7](https://stolichki.ru/clubs/beauty/skin_care/sklerodermiya).\n\n## Симптомы\nСимптоматика склеродермии разнообразна и зависит от формы и стадии заболевания [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). Некоторые проявления: \n* **Кожные**: уплотнение и утолщение кожи, ограничение подвижности кожи и суставов, изменение пигментации (гиперпигментация или депигментация), появление телеангиэктазий (сосудистых звёздочек) [5](https://uteka.ru/articles/bolezni/sklerodermiya-prichini-simptomi-i-lechenie/). \n* **Сосудистые**: феномен Рейно (спазм сосудов пальцев рук и ног), изменение цвета кожи (бледность, синюшность, покраснение) [5](https://uteka.ru/articles/bolezni/sklerodermiya-prichini-simptomi-i-lechenie/). \n* **Системные проявления**: утомляемость и слабость, потеря веса [5](https://uteka.ru/articles/bolezni/sklerodermiya-prichini-simptomi-i-lechenie/). \n* **Поражение внутренних органов**: фиброз лёгких (затруднённое дыхание, одышка), нарушение функции пищевода (дисфагия, рефлюкс), поражение сердца (миокардит, перикардит), нарушение работы почек (почечный криз) [5](https://uteka.ru/articles/bolezni/sklerodermiya-prichini-simptomi-i-lechenie/).\n\n## Диагностика\nДиагностика склеродермии включает комплексный подход, включающий лабораторные и инструментальные методы исследования [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). Некоторые исследования: \n* **Лабораторные анализы**: определение аутоантител, общих показателей воспаления, например, скорости оседания эритроцитов (СОЭ) [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/). \n* **Инструментальная диагностика**: капилляроскопия ногтевого ложа для оценки состояния мелких сосудов, рентген и компьютерная томография лёгких для выявления фиброза или лёгочной гипертензии [1](https://www.accuniq.ru/support/blog/zdorove/sklerodermiya-simptomy-i-diagnostika/).\n\n## Лечение\n**Полностью излечиться от склеродермии нельзя**, но с помощью методов современной медицины можно добиться ремиссии — состояния, при котором стихают симптомы болезни [4](https://www.fdoctor.ru/bolezn/sklerodermiya/). В лечении применяют препараты, воздействующие на иммунную систему, которые подавляют развитие воспалительного процесса и замедляют разрушение тканей [4](https://www.fdoctor.ru/bolezn/sklerodermiya/). 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