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Такие дефекты затрагивают структуру сердца (например, перегородки между камерами), клапаны или крупные сосуды (аорту и венозные протоки) [4](https://mc21.ru/articles/vrozhdennye-poroki-serdtsa-vps/). \n\nНекоторые виды ВПС: \n* **Дефект межпредсердной перегородки (ДМПП)** — отверстие между правым и левым предсердием [3](https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/). \n* **Дефект межжелудочковой перегородки (ДМЖП)** — отверстие между правым и левым желудочками [3](https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/). \n* **Открытый артериальный проток (ОАП)** — сосуд, функционирующий у плода и соединяющий лёгочную артерию с аортой [3](https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/). В норме закрывается вскоре после рождения, но если этого не происходит, кровь продолжает сбрасываться из аорты в лёгочные сосуды, что со временем перегружает их и сердце [3](https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/).\n\n\n\n## Причины\nТочная причина ВПС не определена, предполагается роль различных внешних факторов и внутренних влияний на организм на ранних сроках беременности [8](https://www.smclinic-spb.ru/zabolevaniya/porok-serdtsa). Некоторые факторы: \n* хромосомные и генные мутации [8](https://www.smclinic-spb.ru/zabolevaniya/porok-serdtsa); \n* внутриутробное инфицирование зародыша [8](https://www.smclinic-spb.ru/zabolevaniya/porok-serdtsa); \n* алкогольные, никотиновые, лекарственные интоксикации в ранних сроках беременности [8](https://www.smclinic-spb.ru/zabolevaniya/porok-serdtsa); \n* серьёзные болезни матери — диабет, аутоиммунные патологии, нарушения свёртывания, эндокринные патологии, нарушения обмена веществ [8](https://www.smclinic-spb.ru/zabolevaniya/porok-serdtsa).\n\n## Симптомы\nПроявления ВПС зависят от их типа и степени тяжести [4](https://mc21.ru/articles/vrozhdennye-poroki-serdtsa-vps/)[9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/). Некоторые признаки: \n* **Цианоз** — синюшность кожи и слизистых оболочек, вызванная недостатком кислорода в крови [9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/). \n* **Одышка и учащённое дыхание** — особенно во время кормления или сна [9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/). \n* **Быстрая утомляемость** [9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/). \n* **Плохой набор массы тела** — несмотря на достаточное питание, при пороках сердца ребёнок может не набирать вес [9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/). \n* **Отёки** — при некоторых формах ВПС отекает лицо, ноги, руки или даже всё тело [9](https://gutaclinic.ru/articles/kak-zapodozrit-vrozhdennyy-porok-serdtsa-u-mladentsa/).\n\n## Диагностика\nДля диагностики ВПС используют, например: \n* **Эхокардиографию (УЗИ сердца)** — основной метод, позволяет оценить структуру сердца, размеры камер, состояние клапанов, толщину стенок и движение крови [1](https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/)[12](https://premium-clinic.ru/kak-diagnostiruyutsya-vrozhdennye-poroki-serdtsa-u-detey/). \n* **Электрокардиографию (ЭКГ)** — помогает выявить нарушения сердечного ритма и проводимости, которые могут сопровождать ВПС [1](https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/). \n* **Рентгенографию грудной клетки** — может показать увеличение размеров сердца и признаки застоя в лёгких [1](https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/).\n\n## Лечение\nЛечение ВПС зависит от типа порока, его тяжести и общего состояния ребёнка [1](https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/). Некоторые методы: \n* **Медикаментозная терапия** — некоторые пороки могут быть компенсированы с помощью лекарственных препаратов, которые помогают снизить нагрузку на сердце, улучшить кровообращение и предотвратить осложнения [13](https://irkgpc.gosuslugi.ru/novosti/diagnostika-i-lechenie-vrozhdennyh-porokov-serdtsa-u-novorozhdennyh.html). \n* **Хирургическое лечение** — для сложных пороков сердца может потребоваться открытая операция [13](https://irkgpc.gosuslugi.ru/novosti/diagnostika-i-lechenie-vrozhdennyh-porokov-serdtsa-u-novorozhdennyh.html). В зависимости от конкретного типа дефекта выполняются разные виды операций, такие как устранение дефекта межжелудочковой перегородки, коррекция клапанов или создание обходных путей для восстановления нормального кровообращения [13](https://irkgpc.gosuslugi.ru/novosti/diagnostika-i-lechenie-vrozhdennyh-porokov-serdtsa-u-novorozhdennyh.html). \n* **Пересадка сердца** — в редких и очень сложных случаях, когда другие методы не помогают [13](https://irkgpc.gosuslugi.ru/novosti/diagnostika-i-lechenie-vrozhdennyh-porokov-serdtsa-u-novorozhdennyh.html).","linksData":[{"sourceId":1,"url":"https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/","shownUrl":"https://dzhmao.ru/info/articles/vrozhdennyy-porok-serdtsa-u-novorozhdennykh-kogda-serdtse-betsya-inache/","title":"Врожденный порок сердца у новорожденных: когда сердце бьется иначе","shortUrl":"dzhmao.ru","isTranslated":false,"description":"","greenUrl":"dzhmao.ru"},{"sourceId":2,"url":"https://gemotest.ru/info/spravochnik/zabolevaniya/vrozhdyennye-poroki-serdtsa/","shownUrl":"https://gemotest.ru/info/spravochnik/zabolevaniya/vrozhdyennye-poroki-serdtsa/","title":"Врождённые пороки сердца (ВПС) — что это, причины, симптомы, классификация","shortUrl":"gemotest.ru","isTranslated":false,"description":"","greenUrl":"gemotest.ru"},{"sourceId":3,"url":"https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/","shownUrl":"https://Medgorod-clinic.ru/stati/vrozhdyennye-poroki-serdtsa--diagnostika--lechenie-i-prognozy/","title":"Врождённые пороки сердца: диагностика, лечение и прогнозы.","shortUrl":"Medgorod-clinic.ru","isTranslated":false,"description":"","greenUrl":"Medgorod-clinic.ru"},{"sourceId":4,"url":"https://mc21.ru/articles/vrozhdennye-poroki-serdtsa-vps/","shownUrl":"https://mc21.ru/articles/vrozhdennye-poroki-serdtsa-vps/","title":"Врождённые пороки сердца (ВПС) — структурные отклонения сердца у новорожденных, диагностика и современное лечение кардиоваскулярных аномалий","shortUrl":"mc21.ru","isTranslated":false,"description":"","greenUrl":"mc21.ru"},{"sourceId":5,"url":"https://detskiy-medcentr-spb.ru/disease/vrozhdennyy-porok-serdtsa/","shownUrl":"https://detskiy-medcentr-spb.ru/disease/vrozhdennyy-porok-serdtsa/","title":"Врожденный порок сердца (ВПС) у детей - фазы болезни, причины, лечение | Детская кардиология СМ-Клиники в Санкт-Петербурге","shortUrl":"detskiy-medcentr-spb.ru","isTranslated":false,"description":"","greenUrl":"detskiy-medcentr-spb.ru"},{"sourceId":6,"url":"https://yandex.ru/health/turbo/articles?id=5612","shownUrl":"https://yandex.ru/health/turbo/articles?id=5612","title":"Причины врожденных пороков сердца у детей: новые исследования","shortUrl":"yandex.ru","isTranslated":false,"description":"","greenUrl":"yandex.ru"},{"sourceId":7,"url":"https://ProBolezny.ru/vrozhdennyy-porok-serdca/","shownUrl":"https://ProBolezny.ru/vrozhdennyy-porok-serdca/","title":"Врождённый порок сердца: причины, симптомы и лечение в статье терапевта Кокорина Е. 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