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Чаще всего развивается как следствие воспалительных процессов или дистрофии лёгочной ткани [2](https://doct.ru/diseases/pnevmoskleroz.html). \n\nВыделяют два вида пневмосклероза по распространённости процесса [5](https://uteka.ru/articles/bolezni/pnevmoskleroz/): \n1. **Ограниченный (локальный)** — поражается участок лёгкого [5](https://uteka.ru/articles/bolezni/pnevmoskleroz/). \n2. **Диффузный** — поражается практически весь объём органа, в котором образуется множество мелких очагов рубцовых изменений [2](https://doct.ru/diseases/pnevmoskleroz.html)[5](https://uteka.ru/articles/bolezni/pnevmoskleroz/).\n\n\n\n## Причины\nВ большинстве случаев пневмосклероз развивается в виде осложнения других патологий [2](https://doct.ru/diseases/pnevmoskleroz.html). Некоторые причины: \n* недолеченные пневмонии (вирусные, бактериальные, грибковые или аспирационные) [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* туберкулёз [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* хронический бронхит, поздние стадии ХОБЛ [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* пневмокониоз — длительное вдыхание воздуха, насыщенного токсичной пылью, газами [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* лучевые поражения [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* хронические плевриты, ателектазы [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* долговременное пребывание инородных тел в бронхах [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* наследственные патологии, затрагивающие дыхательную систему [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* травмы, проникающие ранения грудной клетки [2](https://doct.ru/diseases/pnevmoskleroz.html).\n\n## Симптомы\nНа начальных стадиях патология практически не проявляет себя [2](https://doct.ru/diseases/pnevmoskleroz.html). Некоторые симптомы: \n* одышка — вначале развивается только при физических нагрузках, но по мере усугубления состояния появляется и в покое [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* синюшность кожи из-за ухудшения насыщения крови кислородом [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* признаки хронического бронхита: постоянный беспокоящий кашель, сопровождающийся отделением гнойной мокроты [2](https://doct.ru/diseases/pnevmoskleroz.html); \n* при длительном течении патологии — характерный признак дыхательной недостаточности — пальцы Гиппократа [2](https://doct.ru/diseases/pnevmoskleroz.html).\n\n## Диагностика\nДля постановки диагноза назначают инструментальные исследования [2](https://doct.ru/diseases/pnevmoskleroz.html): \n* **Рентгенография** — позволяет выявить степень поражения и характер распространения фиброзных очагов [2](https://doct.ru/diseases/pnevmoskleroz.html). \n* **Бронхография** — методика изучения бронхиального древа, позволяет выявить отклонения в структуре бронхов, изменение их формы и проходимости [2](https://doct.ru/diseases/pnevmoskleroz.html). \n* **Спирометрия** — позволяет оценить функциональное состояние дыхательной системы, степень дыхательной недостаточности и проходимость бронхов [2](https://doct.ru/diseases/pnevmoskleroz.html). \n* **МРТ** — используется для детальной диагностики, позволяет подробно исследовать поражённые участки лёгких [2](https://doct.ru/diseases/pnevmoskleroz.html).\n\n## Лечение\n**Основная цель лечения** — устранение фактора, который привёл к развитию болезни [3](https://bogolubov.center/about/news/articles/pnevmoskleroz). Некоторые методы терапии: \n* **Терапия патологии, ставшей причиной пневмосклероза** [11](https://www.invitro.ru/library/bolezni/32491/). \n* **Приём симптоматических препаратов**: противокашлевых, муколитиков (для улучшения отхождения мокроты), противовоспалительных [11](https://www.invitro.ru/library/bolezni/32491/). \n* **Хирургическое лечение** — удаление поражённой части лёгкого позволяет частично восстановить дыхательную функцию и предупредить прогрессирование заболевания [11](https://www.invitro.ru/library/bolezni/32491/). \n\n**Лечением пневмосклероза занимается врач-пульмонолог** [3](https://bogolubov.center/about/news/articles/pnevmoskleroz). 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